severe combined immunodeficiency disease

January 2005
Taber's Cyclopedic Medical Dictionary;2005, p1981
Reference Entry
A definition of "severe combined immunodeficiency disease" is presented. It refers to a syndrome in which both humoral and cell-mediated immunity get functionally impaired and the patient becomes susceptible to fungal, bacterial, and viral infections. The syndrome is commonly inherited and transmitted as an X-linked or autosomal recessive trait. It can be cured by the transplantation of bone marrow or fetal liver as a source of stem cells.


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