First Description of Coronary Artery Ostial Atresia With Fistulous Origin From a Normal Right Ventricle

Olabiyi, Olawale; Kearney, Debra; Krishnamurthy, Rajesh; Morales, David; Cabrera, Antonio G.
December 2013
Pediatric Cardiology;Dec2013, Vol. 34 Issue 8, p1877
Academic Journal
Case Study
Anomalous origins of both the left and right coronary arteries are rare but have been well documented when both arteries arise from the pulmonary trunk (Angelini et al., Circulation 105:2449–2454, 2002 ). An anomalous coronary arterial origin from the pulmonary arteries usually involves the left coronary artery (ALCPA) and less frequently the right coronary artery (ARCPA). At least three cases have been reported in which the right coronary artery arose abnormally from the left ventricle (LV), but none have been reported in which both coronary arteries took their origin from the right ventricle (Ippisch and Kimball, J Am Soc Echocardiogr 23:222.e1–222.e2, 2010 ; Okuyama et al., Jpn Heart J 36:115–118, 1995 ; Culbertson et al., Pediatr Cardiol 16:73–75, 1995 ). Ostial atresia with anomalous origin of a coronary artery from the right ventricle has been described only in pulmonary atresia with an intact ventricular septum and a hypoplastic right ventricle. In this setting, atresia of both coronary ostia with right ventricular origin of both coronary arteries is a rare variant. This report presents a neonate in whom the entire coronary arterial system arose from the right ventricle via a single fistula with no other intracardiac defects. To the authors’ knowledge, this anomaly has not been described previously.


Related Articles

  • An Angiographic Predictor of Pulmonary Artery Stenosis After the Norwood-Sano Operation for Hypoplastic Left Heart Syndrome. Seckeler, Michael; Mery, Carlos; Gangemi, James; Peeler, Benjamin; Jayakumar, K. // Pediatric Cardiology;Dec2012, Vol. 33 Issue 8, p1281 

    The objective of this study was to determine angiographic predictors of future pulmonary artery stenosis (PS) in patients with hypoplastic left heart syndrome (HLHS) at the time of pre-stage 2 cardiac catheterization (PS2C). The Sano modification of the Norwood operation (NSO) for HLHS includes...

  • Impact of right ventricle–pulmonary artery conduit placement on pulmonary artery development after the Norwood procedure in hypoplastic left heart syndrome†. Kołcz, Jacek; Składzień, Tomasz; Kordon, Zbigniew; Rudziński, Andrzej; Skalski, Janusz // European Journal of Cardio-Thoracic Surgery;Aug2012, Vol. 42 Issue 2, p218 

    OBJECTIVES The right ventricle-to-pulmonary artery (RV–PA) shunt in the Norwood procedure (NP) for children with hypoplastic left heart syndrome (HLHS) provides stable haemodynamics and improves interstage survival. The aim of the study was to find the effect of RV–PA placement on...

  • 93510 and More Make Way for New 2011 Coronary Codes.  // Cardiology Coding Alert;Aug2011, Vol. 14 Issue 8, p51 

    The article presents a case study on the 2011 coronary codes. It notes several heart procedures including selective coronary angiography, right and left coronary arteries, and contrast ventriculography with left heart catheterization. It elaborates on indications of such diseases and the...

  • Absence of the coronary sinus with coronary venous drainage into the main pulmonary artery. Ogawa, Kiyoshi; Hishitani, Takashi; Hoshino, Kenji // Cardiology in the Young;Oct2013, Vol. 23 Issue 5, p759 

    We describe the case of a 9-year-old girl demonstrating isolated absence of the coronary sinus with abnormal coronary venous drainage into the main pulmonary artery. Coronary angiography showed normal coronary arterial trees and contrast medium from both coronary arteries drained into the main...

  • Arrhythmogenic right ventricular dysplasia presenting as acute coronary syndrome: a case report. Khalil, Siddiq I.; Kamal, Amjad; Ahmad, Shakeel // European Journal of Echocardiography;2004, Vol. 5 Issue 5, p394 

    Arrhythmogenic right ventricular dysplasia (ARVD) is underdiagnosed cardiomyopathy which commonly presents in young adults with ventricular tachycardia or sudden death. We report a case of ARVD presenting with features of acute coronary syndrome. The suspicion of ARVD came only when...

  • Single Coronary Ostium in Right Coronary Sinus: Previously Unreported "One for All" Configuration. Njeim, Mario; Nasr, Youssef; Younes, Mohamad; Song, Thomas K.; Koenig, Gerald C.; Nour, Khaled // Texas Heart Institute Journal;Dec2014, Vol. 41 Issue 6, p601 

    We report our identification of a single coronary ostium arising from the right coronary sinus of Valsalva, in a 63-year-old woman who presented with chest pain atypical of angina. Coronary angiograms showed that the left anterior descending coronary artery arose from a right ventricular branch...

  • Mending broken hearts. Clarke, Gemma // Synergy: Imaging & Therapy Practice;Sep2012, p4 

    The article discusses some of the procedures undertaken to treat congenital heart defect Hypoplastic Left Heart Syndrome (HLHS) in infants and young children, including the innovative Hybrid procedure at the Evelina Children's Hospital in London, Great Britain. Traditionally, reconstruction for...

  • Hypoplastic Left Heart Syndrome: A Handbook for Parents. Jarvis, Mary J. // Library Journal;1/1/1997, Vol. 122 Issue 1, p134 

    Reviews the book `Hypoplastic Left Heart Syndrome: A Handbook for Parents,' by Anna Marie Jaworski.

  • Congenital absence of the right coronary artery with a unique origin of the artery to the sinu-atrial node: A case study. Elliott, Gail Elizabeth; Martin, Alexander Hamilton // International Journal of Anatomical Variations;2012, Vol. 5, p120 

    A 67 year-old female, presented with an absent right coronary artery during dissection in the Gross Anatomy Laboratory, Ross University School of Medicine. This is a previously undocumented origin of the right anterior atrial artery and a unique origin of the sinu-atrial node artery. Although...


Read the Article


Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics