Isolated Total Anomalous Systemic Venous Drainage in an Adult: Case Report

Devendran, Vimalarani; Varghese, Roy; Gudeboyana, Krishnaya; Jessudian, Vimala
December 2013
Pediatric Cardiology;Dec2013, Vol. 34 Issue 8, p1918
Academic Journal
Case Study
Total anomalous systemic venous drainage is a rare form of congenital heart disease. All the systemic venous flow from the body (i.e., from the superior vena cava, inferior vena cava, and coronary sinus) drains abnormally into the left atrium. This condition requires the presence of a left-to-right shunt (atrial septal defect, patent ductus arteriosus, or ventricular septal defect) to allow the systemic venous return to reach the pulmonary circulation. This disorder may be associated with heterotaxy syndromes. This report describes a patient with unique total anomalous systemic venous drainage that was successfully corrected surgically.


Related Articles

  • Sternal Cleft associated with Patent Ductus Arteriosus, Atrial Septal Defect, and Subglottic Hemangioma: A Rarity. Sadeghian, Naser; Mirshemirani, Alireza; Sadeghian, Irandokht // APSP Journal of Case Reports;2014, Vol. 5 Issue 1, p1 

    We present a 2-day-old female neonate with cleft of the upper sternum, patent ductus arteriosus (PDA), atrial septal defect (ASD), and subglottic hemangioma. Dimensional and Doppler echocardiography, abdominal ultrasonography, and imaging were performed. She underwent a surgical repair of...

  • Papillary fibroelastoma associated with congenital heart disease: a coincidental association or a potential new syndrome? Özkan, Mehmet; Astarcıoğlu, Mehmet Ali; Gündüz, Sabahattin; Tuncer, Altuğ // Anatolian Journal of Cardiology / Anadolu Kardiyoloji Dergisi;Nov2015, Vol. 15 Issue 11, p951 

    The article presents several case studies of cardiac papillary fibroelastomas (PFs). Topics discussed include case of PF associated with ostium secundum-type atrial septal defect (ASD); case of PF associated with patent ductus arteriosus (PDA); and presence of congenital heart diseases alert the...

  • Complex TAPVC-Experience with Six Patients. Karthekeyan, Baskar Ranjith; Thangavelu, Periyasamy; Rethinasamy, Jebaraj; Vakamudi, Mahesh; Muthukumar, Siva; Kodali, Rajeshkumar; Sambandham, Kamalakannan; Nandipati, Sushma // Surgical Science;Nov2013, Vol. 4 Issue 11, p509 

    Total anomalous pulmonary venous connection becomes a totally different subset when associated with complex congenital anomalies. The combination of two separate life-threatening congenital heart defects complicates the management of these patients. Six patients with total anomalous pulmonary...

  • Superior repair: A useful approach for some anatomic variants of total anomalous pulmonary venous connection. Okonta, Kelechi E.; Agarwal, Vijay; Abubakar, Umar // African Journal of Paediatric Surgery;Apr-Jun2013, Vol. 10 Issue 2, p131 

    Background: Total anomalous pulmonary venous connection (TAPVC) occurs when all the four pulmonary veins drain to the right atrium or to tributaries of the systemic veins. There have been various published techniques for the repair but none has been agreed on for the different anatomical...

  • Anomalous pulmonary venous connection to superior vena cava: Warden technique. Kottayil, Brijesh P.; Dharan, Baiju S.; Menon, Sabarinath; Bijulal, Sasidharan; Neema, Praveen Kumar; Gopalakrishnan, Shyamkrishnan K.; Jayakumar, Karunakaran // European Journal of Cardio-Thoracic Surgery;Mar2011, Vol. 39 Issue 3, p388 

    Abstract: Objective: Repair of anomalous pulmonary venous connection (APVC) to superior vena cava (SVC) with internal pericardial patch may be complicated by the obstruction of the SVC or pulmonary veins and sinus node dysfunction. Moreover, the shrinkage of the pericardium may lead to late...

  • Totally anomalous pulmonary venous connection directly to the superior caval vein. Giamberti, Alessandro; Deanfield, John E.; Anderson, Robert H.; de Leval, Marc R. // European Journal of Cardio-Thoracic Surgery;Mar2002, Vol. 21 Issue 3, p474 

    Objective: Totally anomalous pulmonary venous connection directly to the superior caval vein is unusual. It is frequently associated with major congenital heart defects such as the syndrome of right isomerism. While improved results have been reported recently for the isolated form, complex...

  • Perioperative management of a neonate presenting with midgut volvulus and obstructed infracardiac total anomalous pulmonary venous connection. Juvekar, Nilesh M.; Deshpande, Sharmila S.; Pratap, Usha; Jagtap, Ranjit R.; Patankar, Shreeprasad P. // Annals of Cardiac Anaesthesia;Jan2011, Vol. 14 Issue 1, p62 

    A letter to the editor is presented about the clinical case of a 17-day-old female child diagnosed with midgut volvulus and obstructed infracardiac total anomalous pulmonary venous connection.

  • Complete Heart block during right IJV cannulation An unusual complication: 2 Different Cases. Singh, Kanwar Vishal; Sahoo, Tapas Kumar; Kharche, Tushar; Dewoolkar, L. V.; Kane, Deepa; Rao, Sangeeta // Internet Journal of Anesthesiology;2007, Vol. 13 Issue 2, p24 

    Heart block and arrhythmia are complications of pulmonary artery and cardiac catheterization. Injury to the conducting system of the heart more often involves the right bundle causing right bundle branch block (RBBB)7 but complete heart block (CHB) can also result. After trauma, impairment of...

  • Persistent Pulmonary Artery Hypertension Following Supracardiac Total Anomalous Pulmonary Venous Connection Repair. Kumar, B.; Mutu, R.; Puri, G. D.; Anju Singh; Rana, S. S. // PVRI Review;Jul-Dec2010, Vol. 2 Issue 3, p126 

    We report a case of supracardiac total anomalous pulmonary venous connection (TAPVC) with persistent post operative pulmonary hypertension unresponsive to sildenafil. Only after ligation of vertical vein, echocardiography could detect a perimembranous ventricular septal defect (VSD). Following...


Read the Article


Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics