TITLE

Perioperative Management of Pheochromocytoma and Catecholamine-Induced Dilated Cardiomyopathy in a Pediatric Patient

AUTHOR(S)
Kalra, Yuvraj; Agarwal, Hemant S.; Smith, Andrew H.
PUB. DATE
December 2013
SOURCE
Pediatric Cardiology;Dec2013, Vol. 34 Issue 8, p2013
SOURCE TYPE
Academic Journal
DOC. TYPE
Case Study
ABSTRACT
Dilated cardiomyopathy resulting from pheochromocytoma-mediated catecholamine excess poses a unique challenge to heart failure management. Although early screening of patients with familial neoplastic syndromes at risk for pheochromocytoma may facilitate early resection, the resultant manifestations of prolonged catecholamine excess among patients with undiagnosed pheochromocytoma may lead to myocardial fibrosis with both systolic and diastolic dysfunction. Furthermore, the hemodynamic effects of catecholamine excess exacerbate the risks of perioperative hemodynamic instability in the setting of such myocardial depression. This report describes an approach to the perioperative care of a child who had pheochromocytoma and catecholamine-induced cardiomyopathy with ventricular dysfunction refractory to medical management.
ACCESSION #
91907313

 

Related Articles

  • Verteporfin.  // Reactions Weekly;10/29/2011, Issue 1375, p30 

    The article describes the case of a 21-year-old man diagnosed with von Hippel-Lindau syndrome, who experienced retinal detachment after receiving verteportin before photodynamic therapy for retinal capillary haemangioblastoma in his left eye.

  • Management of a Case of von Hippel-Lindau for Coronary Artery Bypass Grafting. Verma, Geetanjali S. // Indian Anaesthetists' Forum;Jul2015, Vol. 16 Issue 14/15, p1 

    von Hippel-Lindau (VHL) disease is a rare autosomal dominant genetic disorder with retinal and nervous system haemangioblastomas, phaeochromocytoma, renal, pancreatic and endolymphatic tumours. These patients usually present for surgeries involving cerebellar or adrenal tumours. In this article,...

  • A Case of von Hippel-Lindau Disease with Colorectal Adenocarcinoma, Renal Cell Carcinoma and Hemangioblastomas. Su Jin Heo; Choong-kun Lee; Kyu Yeon Hahn; Gyuri Kim; Hyuk Hur; Sung Hoon Choi; Kyung Seok Han; Arthur Cho; Minkyu Jung // Cancer Research & Treatment;2016, Vol. 48 Issue 1, p409 

    von Hippel-Lindau (VHL) disease is an autosomal dominant inherited tumor syndrome associated with mutations of the VHL tumor suppressor gene located on chromosome 3p25. The loss of functional VHL protein contributes to tumorigenesis. This condition is characterized by development of benign and...

  • Inhibin-expressing clear cell neuroendocrine tumor of the ampulla: an unusual presentation of von Hippel-Lindau disease. Gucer, Hasan; Szentgyorgyi, Eva; Ezzat, Shereen; Asa, Sylvia; Mete, Ozgur // Virchows Archiv;Oct2013, Vol. 463 Issue 4, p593 

    von Hippel-Lindau (VHL) disease is a hereditary autosomal dominant disorder associated with deletions or mutations in the VHL tumor suppressor gene. Characteristically, up to 60 % of neuroendocrine tumors (NETs) associated with VHL disease display a spectrum of clear cell morphology including...

  • An unusual case of paraganglioma. Sridhar, S.; Parghi, V. // Indian Journal of Endocrinology & Metabolism;Nov/Dec2013, Vol. 17 Issue 6, p1124 

    Pheochromocytomas or Paragangliomas are neroendocrine tumors elaborating catecholamines. They may not present always in a classic manner and a high degree of suspicion is important in diagnosing them early. They can grow large enough to impinge on the great vessels and yet symptoms may not...

  • Anesthetic management of a missed pheochromocytoma during exploratory laparotomy. Suryawanshi, Chhaya; Thatte, W. S.; Chari, V. R. R.; Sapate, Manisha; Goyal, Anuja A. // Anaesthesia, Pain & Intensive Care;Sep-Dec2013, Vol. 16 Issue 3, p296 

    Pheochromocytomas are highly vascular and catecholamine producing tumours derived from sympathetic or parasympathetic nervous system, and are estimated to occur in 2-8 out of 1 million population per year; about 0.1% of all hypertensives harbour a pheochromocytoma. Patients usually present with...

  • Metoclopramide.  // Reactions Weekly;Feb2015, Vol. 1538 Issue 1, p162 

    The article presents a case study of a 32-year-old woman who developed Takotsubo like cardiomyopathy related to phaeochromocytoma after receiving metoclopramide. It describes the condition of the patient who was presented for a planned Caesarean section at 38 weeks under spinal anaesthesia. It...

  • Advanced renal cell carcinoma associated with von Hippel-Lindau disease: A case report and review of the literature. LEI ZHANG; BIN XU; YIDUO WANG; CHUNHUI LIU; KAI LU; YEQING HUANG; NING LIU; XIAOWEN ZHANG; SHUQIU CHEN; MING CHEN // Oncology Letters;Aug2015, Vol. 10 Issue 2, p1087 

    The autosomal dominant hereditary disorder von Hippel-Lindau (VHL) disease is caused by a germline mutation in the VHL gene. The symptoms of VHL include hemangioblastoma of the central nervous system, retinal angiomas, visceral tumors and multiple visceral cysts. However, advanced renal cell...

  • Exclusión prenatal del síndrome de von Hippel-Lindau en una familia mexicana con una mutación nueva en el gen VHL. Chacón-Camacho, Oscar Francisco; Benítez-Granados, Jesús; Zenteno, Juan Carlos // Ginecologia y Obstetricia de Mexico;Apr2013, Vol. 81 Issue 4, p206 

    Von Hippel-Lindau syndrome is an autosomal dominant and familial multisystemic syndrome that is caused by the inactivation of the VHL gene and it is characterized by diverse types of high vasculated tumors of benign and malign nature. This paper reports the clinical characteristics and prenatal...

Share

Read the Article

Courtesy of THE LIBRARY OF VIRGINIA

Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics