TITLE

Kartagener's syndrome: A case series

AUTHOR(S)
Mishra, Mayank; Kumar, Naresh; Jaiswal, Ashish; Verma, Ajay K.; Kant, Surya
PUB. DATE
October 2012
SOURCE
Lung India;Oct-Dec2012, Vol. 29 Issue 4, p366
SOURCE TYPE
Academic Journal
DOC. TYPE
Case Study
ABSTRACT
Kartagener's syndrome is a rare, autosomal recessive genetic ciliary disorder comprising the triad of situs inversus, chronic sinusitis, and bronchiectasis. The basic problem lies in the defective movement of cilia, leading to recurrent chest infections, ear/nose/throat symptoms, and infertility. We hereby report three unusual cases of this rare entity - an infertile male with azoospermia in whom Bochdalek's diaphragmatic hernia coexisted, another case of an infertile female, and a third of an infertile male with oligospermia. The need for a high index of suspicion to make an early diagnosis cannot be overemphasized in such patients so that wherever possible, options for timely treatment of infertility may be offered and unnecessary evaluation of symptoms is avoided.
ACCESSION #
83706146

Tags: CASE studies;  CILIARY body -- Diseases;  SITUS inversus;  SINUSITIS;  BRONCHIECTASIS;  MALE infertility

 

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