Osteomyelitis of Maxilla in Infantile Osteopetrosis: A Case Report with Review of Literature

Balan, Anita; Girija, K. L.; Ranimol, P.
May 2011
International Journal of Clinical Pediatric Dentistry;May-Aug2011, Vol. 4 Issue 2, p125
Academic Journal
Case Study
Osteopetrosis is a rare genetic disorder that causes generalized sclerosis of bone due to a defect in bone resorption and remodeling. It is usually manifesting in two basic forms: An autosomal dominant benign form (osteopetrosis tarda) and an autosomal recessive malignant form (osteopetrosis congenita). A third form, the intermediate recessive type, has also been reported. Dental abnormality may be attributed to pathological changes in bone remodeling. Osteomyelitis is well documented as a complication of osteopetrosis and is severe and difficult to treat. This is a case of 8-year-old boy with osteopetrosis presenting with the complaint of swelling of left side of face.


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