TITLE

Osteopetrosis (Marble Bone Disease): A Rare Disease in Children

AUTHOR(S)
Reddy, M. H. Raghunath
PUB. DATE
September 2011
SOURCE
International Journal of Clinical Pediatric Dentistry;Sep-Dec2011, Vol. 4 Issue 3, p232
SOURCE TYPE
Academic Journal
DOC. TYPE
Case Study
ABSTRACT
Osteopetrosis is a group of diseases that affects the growth and remodeling of bone and characterized by over growth and sclerosis of bone, with thickening of the bony cortices, abnormal dental development and narrowing of the marrow cavities throughout the skeleton. It is an uncommon disease of unknown cause. A 5-year-old boy was suffering from infantile (severe form) osteopetrosis with cardiac enlargement, severe anemia, hepatosplenomagaly and radiographs showed generalized increase in bone density (chalky white), narrowing of skull base is reported here.
ACCESSION #
82736165

 

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