Lymphomatoid Granulomatosis in 10-Month-Old Infant with Lymphopenia: Case Report and Review of the Literature

OZDEMIR, Mehmet Akif; TORUN, Yasemin A.; KARAKUKCU, Musa; KONTAS, Olgun; PATIROGLU, Turkan; YIKILMAZ, Ali
June 2011
International Journal of Hematology & Oncology / UHOD: Uluslarar;Jun2011, Vol. 21 Issue 2, p124
Academic Journal
Case Study
Lymphomatoid granulomatosis (LYG) is an aggresive multiorgan disease that primarily affects the lung but may also involve extrapulmonary sites including the central nervous system, skin, and kidney. The incidence is the highest in middle-aged men and is rare in children. We report a case of LYG involving lung, liver, and skin in a 10-month-old infant who is the youngest patient in the literature.


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