old boy: Hughes Stovin syndrome as a variant of polyarteritis nodosa?

January 2011
Pediatric Rheumatology;2011, Vol. 9 Issue 1, p19
Academic Journal
Case Study
The article presents a case study of an 11-year-old boy with haemoptysis, dyspnoea and weight loss caused by pulmonary vasculitis, leading to pulmonary hypertension. He also appeared to have dural venous sinus thrombosis. It is stated that this presentation might be a rare case of Hughes-Stovin syndrome in childhood. The patient was treated with high-dose steroids and cyclophosphamide pulses. It proposes that this syndrome might be a variant of polyarteritis nodosa.


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