Brain cavernomas associated with en coup de sabre linear scleroderma: Two case reports

January 2011
Pediatric Rheumatology;2011, Vol. 9 Issue 1, p18
Academic Journal
Case Study
The article presents case reports of two patients with brain cavernomas associated with en coup de sabre linear scleroderma (LS). It discusses prevention and treatment of neurological manifestations associated with this condition. In both cases, the cavernomas bled with notable clinical manifestations. It is stated that these two cases emphasize the importance of central nervous system (CNS) imaging in children with en coup de sabre LS.


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