TITLE

Congenital Portal Vein Aneurysm Associated with Peliosis Hepatis and Intestinal Lymphangiectasia

AUTHOR(S)
Mungan, Zeynel; Pinarbasi, Binnur; Bakir, Baris; Gulluoglu, Mine; Baran, Bulent; Akyuz, Filiz; Demir, Kadir; Kaymakoglu, Sabahattin
PUB. DATE
January 2009
SOURCE
Gastroenterology Research & Practice;2009, Vol. 2009, Special section p1
SOURCE TYPE
Academic Journal
DOC. TYPE
Case Study
ABSTRACT
Portal vein aneurisym (PVA), peliosis hepatis (PH) and intestinal lymphangiectasia (IL) all are very uncommon entities. Herein, we presented a unique patient with these three rare entities who was admitted to our hospital because of portal hypertensive ascites rich in protein and lymphocyte. PVA was extrahepatic and associated with coronary vein aneurysm. Peliosis hepatis was of microscopic form. Lymphangiectasia was present in peritoneum and small intestine. Diagnoses of these rare entities were made by imaging techniques and histopathological findings. Patient also had hydronephrosis caused by ureteropelvic junction narrowing. Best of our knowledge, there is no such a case reported previously with the association of PVA, PH and IL. Therefore, we propose PVAPHIL syndrome to define this novel association.
ACCESSION #
55258985

 

Related Articles

  • "Pseudoascites" as a Presenting Physical Sign of Celiac Disease. Granot, Esther; Deckelhaum, Richard J. // American Journal of Gastroenterology;Nov1983, Vol. 78 Issue 11, p730 

    Two children initially referred for evaluation of ascites were diagnosed as suffering from celiac disease. Positive physical signs of ascites were present in the absence of free fluid in the peritioneal cavity. Physical findings of ascites were caused soley by dilated small intestinal loops...

  • PROFILUL CARCINOMATOZELOR PERITONEALE ÃŽN ADENOCARCINOAMELE PANCREATICE. Tiutiuca, R. C.; Tiutiuca, Iuliana // Jurnalul de Chirurgie;2009, Vol. 5 Issue 4, p349 

    Peritoneal carcinosis is a local/regional dissemination of digestive malignancies, gynaecological malignancies or other forms of cancer with or without proof of the existence of systemic metastasis. Mode of formation and evolution is controlled by several factors, mainly physical (the primary...

  • Unusual Presentation of Metastatic Carcinoma to the Small Bowel. Marshak, Richard H.; Lindner, Arthur E.; Kurzban, Jerold; Sicular, Arthur // American Journal of Gastroenterology;Dec1980, Vol. 74 Issue 6, p536 

    Metastatic carcinoma to the small intestine produces a galaxy of roentgen findings including multiple areas of partial intestinal obstruction, ascites, fixation, pleating and thickening of the bowel folds, angulation and nodularity. In the following case the patient presented with a solitary...

  • Treatment and prevention of malignant ascites associated... Loggie, Brian W.; Perini, Mark // American Surgeon;Feb1997, Vol. 63 Issue 2, p137 

    Discusses the treatment and prevention of malignant ascites secondary to nonovarian intra-peritoneal (IP) disseminated maligancies. Relation between the appearance of malignant ascites and cancer; Important objective in the treatment of patients with malignant ascites; Details on the treatment...

  • MDCT and clinicopathological features of small bowel gastrointestinal stromal tumours in 102 patients: a single institute experience. BAHETI, A. D.; SHINAGARE, A. B.; CO'NEILL, A.; KRAJEWSKI, K. M.; HORNICK, J. L.; GEORGE, S.; RAMAIYA, N. H.; TIRUMANI, S. H. // British Journal of Radiology;Sep2015, Vol. 88 Issue 1053, p1 

    Objective: Small bowel (SB) is the second most common site of gastrointestinal stromal tumours (GISTs). We evaluated clinical presentation, pathology, imaging features and metastatic pattern of SB GIST. Methods: Imaging and clinicopathological data of 102 patients with jejunal/ileal GIST treated...

  • Chylous ascytes secondary to acute pancreatitis: a case report and review of literature. Gómez-Martín, J. M.; Martínez-Molina, E.; Sanjuanbenito, A.; Martín-Illana, E.; Arrieta, F.; Balsa, J. A.; Zamarrón, I.; Vázquez, C.; Botella-Carretero, J. I. // Nutricion Hospitalaria;ene/feb2012, Vol. 27 Issue 1, p314 

    Chylous ascites is an uncommon finding which is due to the presence of thoracic or intestinal lymph in the abdominal cavity. It is usually caused by a chronic disruption of the lymphatic system. The present report is one of the rare cases in the literature of chylous ascites secondary to...

  • Prevalence of spontaneous bacterial peritonitis in asymptomatic inpatients with decompensated liver cirrhosis - a pilot study. Kasztelan - Szczerbinska, B.; Słomka, M.; Celinski, K.; Serwacki, M.; Szczerbinski, M.; Cichoz-Lach, H. // Advances in Medical Sciences (De Gruyter Open);2011, Vol. 56 Issue 1, p13 

    Purpose: To assess the prevalence of spontaneous bacterial peritonitis (SBP) in asymptomatic patients with decompensated liver cirrhosis.Material and methods: Patients (pts) with symptoms of decompensation of liver cirrhosis, ascites, and no signs indicating SBP were included to our study....

  • Evaluation and management of chylous ascites. Press, Oliver W.; Ottman, Nancy; Kaufman, Sheldon D.; Press, O W; Press, N O; Kaufman, S D // Annals of Internal Medicine;Mar1982, Vol. 96 Issue 3, p358 

    Twenty-eight cases of chylous ascites occurring over the past 20 years are analyzed for clinical presentation, cause, yield of diagnostic procedure used, and response to therapy. Malignancies were responsible for 21 of 24 adult cases of chyloperitoneum, with lymphomas predominating (13 cases)....

  • Adverse effects of porcine small intestine submucosa implants in experimental ventral hernia repair. Petter-Puchner, A.; Fortelny, R.; Mittermayr, R.; Walder, N.; Öhlinger, W.; Redl, H.; Petter-Puchner, A H; Fortelny, R H; Ohlinger, W // Surgical Endoscopy;Jun2006, Vol. 20 Issue 6, p942 

    Background: Biomeshes made of porcine small intestine submucosa (SIS) have recently been suggested for repair of ventral hernia. A fully biodegradable combination of implant and fibrin sealant fixation was assessed in a new rat model with sutures serving as control.Methods:...

Share

Read the Article

Courtesy of THE LIBRARY OF VIRGINIA

Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics