Tracheal chondrosarcoma -- a rare complication in Maffucci syndrome

Wagnetz, U.; Patsios, D.; Darling, G.; Las Heras, F.; Hwang, D.
September 2009
British Journal of Radiology;Sep2009, Vol. 82 Issue 981, pe178
Academic Journal
Case Study
Maffucci syndrome is a rare congenital non-hereditary disease characterised by subcutaneous haemangiomata and multiple enchondromata. We present a case of an intermediate grade myxoid chondrosarcoma of the tracheal cartilage in a 34-year-old man with a history of Maffucci syndrome. Chondrosarcoma of the trachea are extremely rare tumours. A review of the radiological literature reveals approximately 15 previously published cases. No case was found with a history of Maffucci syndrome.


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