TITLE

Multimodality treatment approach in management of primary peripheral primitive neuroectodermal tumor of the orbit

AUTHOR(S)
Kim, Usha R.; Arora, Vipul; Devanand, J.; Khazei, Hadi M.
PUB. DATE
November 2009
SOURCE
Indian Journal of Ophthalmology;Nov2009, Vol. 57 Issue 5, p395
SOURCE TYPE
Academic Journal
DOC. TYPE
Case Study
ABSTRACT
Primitive neuroectodermal tumor is a small round cell malignancy which rarely involves the orbit. We report a case of a two-year old male child presenting as unilateral eccentric proptosis with extraconal and intraconal mass, diagnosed as primary peripheral primitive neuroectodermal tumor (pPPNET) on histopathology and immunohistochemistry. There is no defined consensus in the management of these tumors due to its rare presentation. We describe its distinguishing features with emphasis on multimodal and aggressive treatment approach which ensures appropriate management of these cases.
ACCESSION #
44058240

 

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