TITLE

Multimodality treatment approach in management of primary peripheral primitive neuroectodermal tumor of the orbit

AUTHOR(S)
Kim, Usha R.; Arora, Vipul; Devanand, J.; Khazei, Hadi M.
PUB. DATE
November 2009
SOURCE
Indian Journal of Ophthalmology;Nov2009, Vol. 57 Issue 5, p395
SOURCE TYPE
Academic Journal
DOC. TYPE
Case Study
ABSTRACT
Primitive neuroectodermal tumor is a small round cell malignancy which rarely involves the orbit. We report a case of a two-year old male child presenting as unilateral eccentric proptosis with extraconal and intraconal mass, diagnosed as primary peripheral primitive neuroectodermal tumor (pPPNET) on histopathology and immunohistochemistry. There is no defined consensus in the management of these tumors due to its rare presentation. We describe its distinguishing features with emphasis on multimodal and aggressive treatment approach which ensures appropriate management of these cases.
ACCESSION #
44058240

 

Related Articles

  • Tumeur fibreuse solitaire de l'orbite: à propos de deux cas avec revue de la littérature. Harmouch, A.; Cherif Chefchaouni, M.; Maher, M.; Sefiani, S. // Oncologie;Oct2010, Vol. 12, p91 

    Solitary fibrous tumour (SFT) is a rare mesenchymal neoplasm that arises most frequently in the pleura and uncommonly involves the orbit. There are 54 cases of solitary fibrous tumour of the orbit reported in the literature. The authors report two cases of an orbital SFT and discuss the...

  • CORE needle biopsy of orbital tumors. Yarovoy, Andrey; Bulgakova, Evgeniya; Shatskikh, Anna; Uzunyan, Dzhulietta; Kleyankina, Svetlana; Golubeva, Olesya // Graefe's Archive of Clinical & Experimental Ophthalmology;Aug2013, Vol. 251 Issue 8, p2057 

    Background: In some orbital mass lesions, histology may be the only way to establish an accurate diagnosis. Core needle biopsy (CNB) is widely performed in oncology, and unlike fine needle aspiration biopsy (FNAB), it can provide sufficient tissue sample for histology and immunohistochemistry....

  • Pulsatile Proptosis in a Metastatic Tumor of the Orbit from Carcinoma Thyroid. Krishnamurthy, Arvind; Vaidhyanathan, Anitha // World Journal of Endocrine Surgery;2010, Vol. 2 Issue 3, p149 

    The article presents a case study of a 64-year-old lady who was diagnosed with pulsatile proptosis. The proptosis was a secondary to the metastatic tumor of the woman's orbit, which was the primary manifestation of thyroid carcinoma. The patient asked for more time before having a thyroid...

  • Orbital liposarcoma masquerading as a hemangioma. Vrcek, Ivan; Hogan, Robert N.; Gilliland, Grant // Baylor University Medical Center Proceedings;Oct2014, Vol. 27 Issue 4, p359 

    The article describes the case of a 67-year old man who was diagnosed with orbital liposarcoma masquerading as a hemangioma. The structural appearance of the tumor is described. Also discussed are the classifications of orbital liposarcoma, its differential diagnoses, and the distinct...

  • Orbital cystic neurinoma. Tokugawa, J.; Nakao, Y.; Mori, K.; Maeda, M. // Acta Neurochirurgica;Jul2003, Vol. 145 Issue 7, p605 

    Summary ¶A 64-year-old woman presented with a 6-month history of exophthalmus of her right eye. She had no neurological deficit except for the exophthalmus and numbness in the right side of her forehead (frontal nerve territory). Neuro-imaging demonstrated a cystic mass in the right orbit....

  • Orbital Space-Occupying Lesions in Indian Children. Bajaj, Mandeep S.; Pushker, Neelam; Chaturvedi, Amrita; Betharia, Subhash M.; Kashyap, Seema; Balasubramanya, Ramamurthy; Sen, Seema // Journal of Pediatric Ophthalmology & Strabismus;Mar/Apr2007, Vol. 44 Issue 2, p106 

    Purpose: To present a review of all patients younger than 16 years who presented to us with orbital space-occupying lesions. Methods: Retrospective case study. Results: We analyzed the records of 119 children younger than 16 years of age who had presented to us with proptosis during the 10-year...

  • A giant malignant hemangiopericytoma of the orbit. Xiao Huang; Ruili Wei; Jiping Cai // Pakistan Journal of Medical Sciences;Oct2010, Vol. 26 Issue 4, p973 

    An 81-year-old man with hemangiopericytoma had clinically conspicuous manifestation of a first slowly then rapidly growing, painless, and sublobe-like mass in the left orbit, proptosis, massive bleeding, and underwent orbital exenteration with keeping the eyelids. The tumor reoccurred 21 months...

  • Orbital roof intradiploic meningioma in a 16-year-old girl. Verma, Satish Kumar; Satyarthee, Gurudutta; Borkar, Sachin Anil; Singh, Manmohan; Sharma, Bhawani Shankar // Journal of Pediatric Neurosciences;Jan-Mar2015, Vol. 10 Issue 1, p51 

    Primary intraosseous or ectopic meningioma of the skull is a rare tumor accounting for about 1% of meningioma. Intradiploic meningioma is an extremely rare type of extraneuraxial meningiomas. Intradiploic meningioma of the orbit is extremely rare, and <8 such cases are reported till date in...

  • A woman with orbital myositis. Shenoy, Chetan; Sattur, Sudhakar // CMAJ: Canadian Medical Association Journal;1/16/2007, Vol. 176 Issue 2, p174 

    The article presents a case study of a 31-year-old woman patient with orbital myositis, the third most common orbital disorder that affects young people. The disease is caused by the thickening of orbital tumors resulting in proptosis, edema of conjunctiva (chemosis) and limited extra-ocular...

Share

Other Topics