Hirayama Disease: Escaping From the Quotidian Imaging

August 2015
Journal of Clinical & Diagnostic Research;Aug2015, Vol. 9 Issue 8, p10
Academic Journal
Case Study
Hirayama disease is a rare type of neurological disease commonly manifesting as brachial monomelic amyotrophy in young males of Asian origin, easily understood as juvenile non-progressive cervical amyotrophy. The first case was reported by Hirayama in 1959. The pathogenesis is attributed towards chronic compression of cervical spinal cord during flexion movements of neck in cases where there is detachment of posterior dura mater. This chronic event, invariably leads to features of cord atrophy along with other MRI features. We report a case of 21-year-old male who presented with atrophy of distal muscles of his right hand and was sent for MRI of cervical spine which revealed prominent posterior epidural venous plexus without significant cord atrophy. Clinico-radiologic profile of the patient leads toward the diagnosis of Hirayama disease which was considered as borderline because of asymmetrical cord atrophy which is a not a routine imaging feature of the entity.


Related Articles

  • Dry spinal tap due to primary psoas and paraspinal abscesses. Ghatak, Tanmoy; Gurjar, Mohan; Kohat, Abhijeet K.; Afzal Azim, Afzal Azim; Hiralal // Saudi Journal of Anaesthesia;Apr-Jun2013, Vol. 7 Issue 2, p215 

    The article presents a case study of a 74-year old teacher presented to the hospital with mild backache and bilateral lower limb weakness for 2 weeks and a high-grade fever for 2 days. Dorsolumbar spine magnetic resonance imaging (MRI) was carried out and reported bilateral psoas abscess,...

  • Cervical spondylotic myelopathy caused by violent motor tics in a child with Tourette syndrome. Ko, Da-Young; Kim, Seung-Ki; Chae, Jong-Hee; Wang, Kyu-Chang; Phi, Ji // Child's Nervous System;Feb2013, Vol. 29 Issue 2, p317 

    Introduction: We report a case of a 9-year-old boy with Tourette syndrome (TS) who developed progressive quadriparesis that was more severe in the upper extremities. Case report: He had experienced frequent and violent motor tics consisting of hyperflexion and hyperextension for years. Magnetic...

  • An Unusual Case of Myelopathy: Surfer's Myelopathy. Dhaliwal, P. P. S.; Cenic, A.; Eesa, M.; du Plessis, S. // Canadian Journal of Neurological Sciences;Mar2011, Vol. 38 Issue 2, p354 

    The article presents a case study of a 29-year-old male surfer who was urgently taken to the hospital due to fainting and paresthesias during his surfing lesson in Hawaii. It states that an investigation using magnetic resonance imaging (MRI) showed an inflammatory reaction on his spinal cord....

  • Spinal Cord Ischemia Secondary to Hypovolemic Shock. Oh, Jacob Y. L.; Kapoor, Siddhant; Koh, Roy K. M.; Yang, Eugene W. R.; Hwan-Tak Hee // Asian Spine Journal;2014, Vol. 8 Issue 6, p831 

    A 44-year-old male presented with symptoms of spinal cord compression secondary to metastatic prostate cancer. An urgent decompression at the cervical-thoracic region was performed, and there were no complications intraoperatively. Three hours postoperatively, the patient developed acute...

  • Isolated cervical intramedullary cysticercosis. Mewada, Tushit; Srivastava, Arvind Kumar // Neurology India;Jan/Feb2016, Vol. 64 Issue 1, p188 

    The article discusses the case of a 43-year-old male patient with an intramedullary cysticercosis in the cervical spinal cord. Topics covered include the presentation of the patient with weakness of the right upper and lower limbs, the results of the magnetic resonance imaging (MRI) of the...

  • Hirayama's disease: The importance of flexion magnetic resonance imaging. Jakhere, S.; Wagh, V. // Journal of Postgraduate Medicine;Jan-Mar2011, Vol. 57 Issue 1, p48 

    Hirayama's disease is a form of juvenile muscular atrophy affecting young individulas in their second to third decade. The underlying pathogenetic mechanism is believed to be an imbalanced growth between the individuals' vertebral column and the spinal canal contents, which causes abutment of...

  • Hirayama Disease in Children From North America. Ghosh, Partha S.; Moodley, Manikum; Friedman, Neil R.; Rothner, A. David; Ghosh, Debabrata // Journal of Child Neurology;Dec2011, Vol. 26 Issue 12, p1542 

    Hirayama disease has been mainly reported from Asia; only a few cases are from the Western hemisphere, particularly North America. This is a retrospective chart review of patients < 18 years, diagnosed with Hirayama disease from a single center over 10 years. We diagnosed 6 children (4 boys),...

  • Pure Spinal Epidural Cavernous Hemangioma with Intralesional Hemorrhage: A Rare Cause of Thoracic Myelopathy. Donghwan Jang; Choonghyo Kim; Seung Jin Lee; Young-Joon Ryu; Jiha Kim // Korean Journal of Spine;2014, Vol. 11 Issue 2, p85 

    Although cavernous hemangiomas occur frequently in the intracranial structures, they are rare in the spine. Most of spinal hemangiomas are vertebral origin and "pure" epidural hemangiomas not originating from the vertebral bone are very rare. Our spinal hemangioma case is extremely rare because...

  • Prenatal diagnosis of split cord malformation by ultrasound and fetal magnetic resonance imaging: case report and review of the literature. Kutuk, Mehmet; Ozgun, Mahmut; Tas, Mustafa; Poyrazoglu, Hatice; Yikilmaz, Ali // Child's Nervous System;Dec2012, Vol. 28 Issue 12, p2169 

    Introduction: Split cord malformation (SCM) is rare congenital disorder of spine in which bony, fibrous, or cartilaginous septum subdivides partially or completely the vertebral canal. SCM can be associated with other spinal abnormalities such as spina bifida, Arnold-Chiari malformation,...


Read the Article


Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics