A rare presentation of subacute sclerosing panencephalitis with acute fulminant course and atypical radiological features

Jain, Rajendra Singh; Sannegowda, Raghavendra Bakki; Srivastava, Trilochan; Jain, Rahul; Mathur, Tarun; Gandhi, Pankaj
October 2013
Annals of Indian Academy of Neurology;Oct2013, Vol. 16 Issue 4, p732
Academic Journal
The article discusses subacute sclerosing panencephalitis (SSPE), which is a progressive, fatal encephalitis of children and adolescents caused by persistent infection of immune resistant measles virus. In the case of a 14-year-old with acute onset rapidly progressive cognitive decline and myoclonic jerks of 15 days duration, magnetic resonance imaging (MRI) showed hypointensities on T1W image with corresponding hyperintensities on T2W image and T2 flair.


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