Lutembacherov sindrom: prikaz slučaja

Biočić, Stanko; Rudan, Diana; Vincelj, Josip
October 2013
Cardiologia Croatica;Oct/Nov2013, Vol. 8 Issue 10/11, p352
Academic Journal
Lutembacher's syndrome refers to a congenital atrial septal defect (ASD) complicated by aquired mitral stenosis (MS). It was first described by Lutembacher, a French physician, in 1916. This syndrome is a very rare disease, it is found that the incidence of Lutembacher's syndrom is 0.001/10,00000. The hemodynamic effects of this syndrome are a result of the interplay between the relative effects of the ASD and MS. We present a 54-year-old female referred to hospital for echocardiographic evaluation of previously diagnosed mild MS. She reported progression of dyspnea over the last month. Two years ago, she was admitted to another hospital because of heart failure and transthoracic echocardiography (TTE) revealed moderate MS with perserved left ventricular systolic function. We performed TTE and transesophageal echocardiogram and found severe MS with ASD that was previously unrecognised. The diagnosis of Lutembacher's syndrome was established. This case demonstrates the presence of this rare disease in our population, but we would also like to stress the importance of the role of echocardiography in identifying many clinical syndromes including this one.


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