Isolated noncompacted left ventricular cardiomyopathy

Wittmann-Price, Ruth A.; Altman-Shaw, Amy
December 2011
British Journal of Cardiac Nursing;Dec2011, Vol. 6 Issue 12, p598
Academic Journal
Isolated noncompacted left-ventricular cardiomyopathy or left-ventricular noncompaction (LVNC) is a specific myopathy that was first recognized 25 years ago. It is congenital in origin and there are important characteristics of the syndrome that distinguish it from other types of cardiomyopathy. The exact genetic transmission is still being investigated. LVNC affects mainly young adults and the diagnosis is often made when the patient presents with symptoms of severe congestive heart failure. The condition can lead to death from heart failure, a thromboembolism, or a fatal arrhythmia. Treatment of this cardiomyopathy is most effective when started early, and consists of preventing heart failure and emboli, and decreasing the incidence of arrhythmias. Identification of affected families is needed as well as research about appropriate treatment modalities. This review aims to increase nurses' awareness of the condition, its diagnosis, and treatments.


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