Akinetic mutism as a classification criterion for the diagnosis of Creutzfeldt-Jakob disease

Otto, Anke; Zerr, Inga; Lantsch, Maria; Weidehaas, Kati; Riedemann, Christian; Poser, Sigrid; Otto, A; Zerr, I; Lantsch, M; Weidehaas, K; Riedemann, C; Poser, S
April 1998
Journal of Neurology, Neurosurgery & Psychiatry;Apr1998, Vol. 64 Issue 4, p524
Academic Journal
journal article
No abstract available.


Related Articles

  • Creutzfeldt-Jakob disease. Behan, P.O. // British Medical Journal (Clinical Research Edition);6/5/1982, Vol. 284 Issue 6330, p1658 

    Focuses on the Creutzfeldt-Jakob disease. Incidence of Creutzfeldt-Jakob disease; Disease symptoms; Usability of laboratory investigations in the diagnosis.

  • Inflammatory Cerebrospinal Fluid in Sporadic Creutzfeldt-Jakob Disease. Bui, Esther; Ehrensperger, Eric; Sahlas, Demetrios J.; Murray, Brian J.; Bergeron, Catherine; Glikstein, Rafael S.; Aviv, Richard; Schipper, Hyman M. // Canadian Journal of Neurological Sciences;Nov2008, Vol. 35 Issue 5, p625 

    Background: Sporadic Creutzfeldt-Jakob disease (CJD) is a fatal, transmissible spongiform encephalopathy characterized by rapidly progressive dementia, myoclonus, ataxia and akinetic mutism. The underlying mechanism is believed to be a conformational change of a native prion protein which...

  • Creutzfeldt–Jakob disease with E200K PRNP mutation: a case report and revision of the literature. Mancuso, Michelangelo; Siciliano, Gabriele; Capellari, Sabina; Orsucci, Daniele; Moretti, Policarpo; Fede, Giuseppe; Suardi, Silvia; Strammiello, Rosaria; Parchi, Piero; Tagliavini, Fabrizio; Murri, Luigi // Neurological Sciences;Oct2009, Vol. 30 Issue 5, p417 

    Creutzfeldt–Jakob disease (CJD) is typically characterized by rapidly progressive dementia and myoclonus, and it is caused by a conformational change of the prion protein. The heritable forms are associated with mutation in the gene encoding the prion protein ( PRNP). We report a...

  • Creutzfeldt-Jakob disease: A great masquerade in neurology, a rare case report from South India. Varadan, Sivaprakash; Singh, Sudagar; Vangipuram, Deepak Rajkumar; Jayachandran, Damodharan // Journal of the Scientific Society;Sep/Oct2015, Vol. 42 Issue 3, p201 

    Creutzfeldt-Jakob disease (CJD) is a rare, fatal neurodegenerative disease caused by an infectious protein called prion and is characterized by spongiform changes, neuronal loss, reactive astrocytic proliferation, and accumulation of pathologic cellular protein. Clinical presentation of CJD is...

  • Multitracer PET imaging in Heidenhain variant of Creutzfeldt–Jakob disease. Thomas, A.; Klein, J. C.; Galldiks, N.; Grond, M.; Jacobs, A. H. // Journal of Neurology;Feb2006, Vol. 253 Issue 2, p258 

    A letter to the editor is presented regarding the effectiveness of multitracer positron emission tomographic imaging in the early diagnosis of Creutzfeldt-Jakob Disease.

  • Creutzfeldt-Jakob disease.  // Columbia Electronic Encyclopedia, 6th Edition;Feb2013, p1 

    Creutzfeldt-Jakob disease: see prion.

  • Creutzfeldt-Jakob disease.  // Columbia Electronic Encyclopedia, 6th Edition;Q1 2017, p1 

    Creutzfeldt-Jakob disease: see prion.

  • Acute presentation of rapidly progressive probable Creutzfeldt-Jakob disease. Harrington, Patrick; Penge, Justin; Mills, Edouard; Ishaque, Ahmed // British Journal of Hospital Medicine (17508460);Mar2013, Vol. 74 Issue 3, p170 

    The article presents the case of a 68-year old man admitted with a 3-week history of cognitive deterioration and progressive gait disturbance. He was pronounced dead after a diagnosis of sporadic Creutzfeldt -- Jakob (CJD) disease because of the rapidity of decline and a progression to akinetic...

  • Early identification of variant Creutzfeldt-Jakob disease. Pocchiari, Maurizio // BMJ: British Medical Journal (International Edition);02/21/98, Vol. 316 Issue 7131, p563 

    Editorial. Provides information on the variant form of Creutzfeldt-Jakob disease which is caused by the same strain of agent as bovine spongiform encephalopathy. Possibility of a definitive diagnosis of the disease; Prediction as to the origin of the disease; Symptoms of Creutzfeldt-Jakob disease.

  • Novel mutation of the PRNP gene of a clinical CJD case. Kotta, Konstantia; Paspaltsis, Ioannis; Bostantjopoulou, Sevasti; Latsoudis, Helen; Plaitakis, Andreas; Kazis, Dimitrios; Collinge, John; Sklaviadis, Theodoros // BMC Infectious Diseases;2006, Vol. 6 Issue 1, p1 

    Background: Transmissible spongiform encephalopathies (TSEs), a group of neurodegenerative diseases, are thought to be caused by an abnormal isoform of a naturally occurring protein known as cellular prion protein, PrPC. The abnormal form of prion protein, PrPSc accumulates in the brain of...


Read the Article


Sign out of this library

Other Topics