TITLE

The neuropathology of phenylketonuria: human and animal studies

AUTHOR(S)
Huttenlocher, Peter R.
PUB. DATE
October 2000
SOURCE
European Journal of Pediatrics. Supplement;2000, Vol. 159, pS102
SOURCE TYPE
Academic Journal
DOC. TYPE
Article
ABSTRACT
Examines the pathologic changes in the brain of untreated phenylketonuria patients. Myelin defect of phenylketonuria; Association between phenylketonuria and leucodystrophy; Impairment in development of cerebral cortex and the concept of critical periods; Histologic studies of the cerebral cortex in animal models of phenylketonuria; Application of special histologic methods to human phenylketonuria material.
ACCESSION #
6102348

 

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