TITLE

Frosted branch angiitis, neuroretinitis as initial ocular manifestation in Behçet disease

AUTHOR(S)
Al-Mujaini, Abdullah; Wali, Upender K.
PUB. DATE
May 2011
SOURCE
Indian Journal of Ophthalmology;May2011, Vol. 59 Issue 3, p240
SOURCE TYPE
Academic Journal
DOC. TYPE
Article
ABSTRACT
Behçet disease is an idiopathic, multisystem disorder characterized by recurrent episodes of orogenital ulceration and vasculitis of the veins and arteries of all calibers. Ocular involvement may affect the conjunctiva, sclera, uveal tract, vitreous, blood vessels, and retina. Many theories have pointed toward an autoimmune response behind its pathogenesis, which may be triggered by exposure to an infectious agent. Frosted branch angiitis is characterized by vascular inflammation, sheathing, retinal edema, and retinal hemorrhages. The disease may be idiopathic in a majority of the cases or may be associated with ocular and systemic pathology. Association between Behçet disease, Frosted branch angiitis, and neuroretinitis is not reported in literature. This uncommon combination reflects the varied systemic and ocular manifestations in Behçet disease, especially in patients who are not diagnosed and treated in time. We hereby report a case of bilateral frosted branch angiitis and neuroretinitis in a young male from Middle-east, suffering from Behçet disease.
ACCESSION #
60948883

 

Related Articles

  • Primary angiitis of the central nervous system. Rehman, H. U. // Journal of the Royal Society of Medicine;Nov2000, Vol. 93 Issue 11, p586 

    The article offers information about the primary angiitis of the central nervous system in Great Britain. The primary angiitis of a nervous system is a rare disease to which the terms granulomatous angiitis and isolated cerebral vasculitis have also been applied. There are primary and secondary...

  • An improved assay for enumeration of circulating endothelial cells. Woywodt, A.; Goldberg, C.; Scheer, J.; Regelsberger, H.; Haller, H.; Haubitz, M. // Annals of Hematology;Aug2004, Vol. 83 Issue 8, p491 

    Circulating endothelial cells have been established as markers of vascular disease, such as small vessel vasculitis, acute vascular rejection in renal transplant recipients, and cyclosporine-induced endothelial damage. Enumeration of these cells by immunomagnetic isolation and acridine staining...

  • Tongue Necrosis, Temporal Arteritis, and Esophageal Carcinoma: Is There a Connection? Mouadeb, Debbie; Campisi, Paolo; Rochon, Louise; Hier, Michael P.; Black, Martin J. // Journal of Otolaryngology;Jan/Feb2004, Vol. 33 Issue 1, p50 

    Temporal or giant cell arteritis is a systemic granulomatous vasculitis that predominantly affects medium and large-sized arteries. This condition more commonly affects women older than 60 years and often presents with headaches and visual symptoms. Although uncommon, it has been recognized that...

  • Determinants of Vessel Targeting in Vasculitis. Hoffman, Gary S. // Clinical & Developmental Immunology;Sep-Dec2004, Vol. 11 Issue 3/4, p275 

    Studies of autoimmune diseases have not yet elucidated why certain organs or vessels become the objects of injury while others are spared- This paper will explore the hypothesis that important differences exist in regions of the aorta that determine vulnerability to diseases, such as...

  • Does Lymphocytic Thrombophilic Arteritis Have a Wider Histopathological Spectrum? A Case Displaying Clinical Features of Macular Arteritis with Histolopathological Features of Lymphocytic Thrombophilic Vasculitis. Noakes, Rowland; Whitehead, Kevin // Clinical Medicine Insights: Dermatology;2012, Issue 5, p9 

    Macular arteritis is a benign condition characterised clinically by livedo racemosa and histopathologically by lymphocytic vasculitis involving the medium sized arterioles. We report a case displaying clinical features of macular arteritis with a lymphocytic vasculitis involving the vessels of...

  • Hearing Loss and Kidney Dysfunction: Finding a Unifying Diagnosis. Iruku, Praveena; Karanth, Puja; Tiu, Hannah; Kankam, Charity; Shaheen, Khaldoon // Case Reports in Medicine;2013, p1 

    Microscopic polyangiitis (MPA) is a systemic vasculitis that affects small caliber vessels, with renal and lung compromise. Diagnosis can be challenging; timely diagnosis and treatment are important to prevent devastating complication, particularly renal failure. We present a case of a patient...

  • Temporal Arteritis.  // New Harvard Guide to Women's Health;2004, p587 

    Presents information and health guide for women about temporal arteritis, a vascular disorder involving inflammation of the large vessels throughout the body. Age of women who are likely to develop temporal arteritis; Symptoms of the disease; Method for evaluating this health condition; Ways to...

  • Takayasu's arteritis in Arabs. Mustafa, Khader // Clinical Rheumatology;Dec2014, Vol. 33 Issue 12, p1777 

    The objective of this study was to describe epidemiological and clinical features of Takayasu's arteritis (TA) among Arab populations and to compare it to other populations. We conducted a systematic review of reports about TA from Arab countries published in English and French until 2013. All...

  • Pediatric-onset Takayasu's arteritis: clinical features and short-term outcome. Misra, Durga; Aggarwal, Amita; Lawrence, Able; Agarwal, Vikas; Misra, Ramnath // Rheumatology International;Oct2015, Vol. 35 Issue 10, p1701 

    The aim of this was to assess clinical features and outcome in pediatric-onset Takayasu's arteritis (TA). Retrospective data analysis of patients diagnosed with TA over last 13 years with onset before 18 years of age was done. Their presenting features, activity (by NIH criteria, ITAS2010,...

Share

Read the Article

Courtesy of THE LIBRARY OF VIRGINIA

Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics