Hyperacusis in Williams Syndrome

Johnson, Liane B.; Comeau, Michel; Clarke, Kevin D.
March 2001
Journal of Otolaryngology;Mar/Apr2001, Vol. 30 Issue 2, p90
Academic Journal
Attempts to define hyperacusis in audioparametric terms through a study of children with Williams syndrome. Presence of persistent hyperacusis in all patients that resulted in varying degrees of interference with daily activities; Absence of transient evoked otoacoustic emissions (TEOAE) in patients with sensorineural hearing loss; Absence of TEOAE despite normal hearing thresholds.


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