Unilateral situs inversus of optic disc associated with reduced binocularity and stereoacuity resembling monofixation syndrome

Kothari, Mihir; Chatterjee, Debapriya N.
March 2010
Indian Journal of Ophthalmology;Mar2010, Vol. 58 Issue 3, p241
Academic Journal
Situs inversus of the optic disc is a rare, usually bilateral, congenital embryological abnormality associated with high myopia, optic disc coloboma or tilted optic disc. It is characterized by emergence of the retinal vessels in an anomalous direction with dysversion of the optic disc. In this report we present a 13-year-old boy diagnosed with isolated, unilateral situs inversus of the optic disc associated with reduced binocularity and stereoacuity resembling a monofixation syndrome. The clinicians should be aware of this association and assess the binocularity in patients with unilateral optic disc or macular anomalies. Conversely, patients with reduced binocularity and stereoacuity should be carefully evaluated for macular or optic nerve anomalies, if not associated with strabismus, anisometropia and eccentric fixation. Typical fundus picture, optical coherence tomography and multifocal electro retinogram of the patient would be instructive to a clinician.


Related Articles

  • Macular Changes Following Strabismus Surgery Confirmed by the Use of Optical Coherence Tomography. Nelson, Leonard B. // Journal of Pediatric Ophthalmology & Strabismus;Jan/Feb2016, Vol. 53 Issue 1, p10 

    The author reflects on a study within the issue where the authors of the study documented subclinical increases in the foveal and perifoveal macular thickness following strabismus surgery using Optical coherence tomography (OCT).

  • Laparoscopic cholecystectomy technique in a patient with situs inversus totalis. Aydın, İbrahim; Pergel, Ahmet; Yücel, Ahmet Fikret; Akdoğan, Remzi Adnan; Şahin, Dursun Ali // Dicle Medical Journal / Dicle Tip Dergisi;2013, Vol. 40 Issue 2, p294 

    Situs inversus totalis is a rare congenital anomaly. It may produce difficulties in diagnosis and therapeutic management of abdominal pathology, particularly in laparoscopic surgery because of the mirror-image anatomy. Here we report a case of situs inversus totalis and cholelithiasis...

  • situs inversus. Peters, Michael // BMA A-Z Family Medical Encyclopedia;2004, p691 

    An encyclopedia entry for "situs inversus" is presented. It refers to an unusual condition in which the internal organs are located in a mirror image of their normal positions. There is no treatment needed given that all the organs are functioning normally.

  • Agnathia Holoprosencephaly and Situs Inversus in A Neonate Born to an Alcoholic Mother. GOSWAMI, DIBYAJYOTI; KUSRE, GIRIRAJ // Journal of Clinical & Diagnostic Research;May2015, Vol. 9 Issue 5, p1 

    Agnathia, holoprosencephaly and situs inversus complex is an extremely rare form of congenital malformation. Though a few cases have been reported from other parts of the world, to the best of our knowledge none has been reported from India so far. Maternal alcoholism is regarded as an important...

  • Optical coherence tomography: a quantitative tool to screen for papilledema in craniosynostosis. Driessen, Caroline; Eveleens, Jordi; Bleyen, Isabel; Veelen, Marie-Lise; Joosten, Koen; Mathijssen, Irene // Child's Nervous System;Jun2014, Vol. 30 Issue 6, p1067 

    Purpose: Our aim was to evaluate if optical coherence tomography (OCT) can be used as an alternative for fundoscopy to screen for increased intracranial pressure (ICP) in children with craniosynostosis Methods: We performed a prospective cohort study at the Dutch Craniofacial Centre. We included...

  • Visualization of vitreomacular tractions with en face optical coherence tomography. Forte, R.; Pascotto, F.; de Crecchio, G. // Eye;Nov2007, Vol. 21 Issue 11, p1391 

    BackgroundIn vitreomacular traction syndrome, an incomplete vitreous detachment with persistent vitreous traction on the macula is present. This condition may determine formation of epiretinal membranes, macular puckering, macular oedema, and traction macular detachment. Recently introduced en...

  • Optical coherence tomography findings in optic disk melanocytoma. Kadıoğlu, Ekrem; Gönül, Şaban; Atalay, Kürşat // Dicle Medical Journal / Dicle Tip Dergisi;2011, Vol. 38 Issue 2, p231 

    A 49 years old male patient admitted to hospital with difficulty in reading. Distant visual acuity, anterior segment examination, and intraocular pressure measurements were normal in his both eyes. The fundus examination was normal in his right eye but in the left eye a pigmented lesion...

  • The Effect of Optic Disc Center Displacement on Retinal Nerve Fiber Layer Measurement Determined by Spectral Domain Optical Coherence Tomography. Shin, Joong Won; Shin, Yong Un; Uhm, Ki Bang; Sung, Kyung Rim; Kang, Min Ho; Cho, Hee Yoon; Seong, Mincheol // PLoS ONE;10/26/2016, Vol. 11 Issue 10, p1 

    Purpose: To investigate the effect of optic disc center displacement on retinal nerve fiber layer (RNFL) measurement determined by spectral domain optical coherence tomography (SD-OCT). Methods: The optic disc center was manipulated at 1-pixel intervals in horizontal, vertical, and diagonal...

  • Posterior staphylomas and scleral curvature in highly myopic children and adolescents investigated by ultra-widefield optical coherence tomography. Tanaka, Noriko; Shinohara, Kosei; Yokoi, Tae; Uramoto, Kengo; Takahashi, Hiroyuki; Onishi, Yuka; Horie, Shintaro; Yoshida, Takeshi; Ohno-Matsui, Kyoko // PLoS ONE;6/10/2019, Vol. 14 Issue 6, p1 

    Purpose: To determine the early signs of posterior staphylomas in highly myopic eyes of younger subjects by swept-source ultra-widefield optical coherence tomography (WF-OCT). Methods: This was an observational case series study. Highly myopic subjects younger than 20 years old who were...


Read the Article


Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics