Zespół Gardnera -- przegląd piśmiennictwa

Sroczyk, Łukasz; Cader, Jan; Więckiewicz, Włodzimierz
May 2009
Gastroenterologia Polska / Gastroenterology;2009, Vol. 16 Issue 3, p248
Academic Journal
This article's aim is to introduce and integrate information about rare genetic disease - Gardner's syndrome. The syndrome was described for the first time at the early 1950s. Typical triad of symptoms for this disease are adenomatous polyposis coli, soft tissue tumors and multiple osteomas. Each of them can occur at different age. Bone tumors occur earlier than intestines polyps, those that may lead directly to intestinal cancer. Evolution of multiple osteomas in mandible may result in disturbances in teeth appearance and their placement in mouth. Dental medical doctor is first, who can diagnose Gardner's syndrome symptoms. Consciousness of seriousness of sickness, demonstrated knowledge about its symptoms, early diagnosis and referring patient to adequate specialist can contribute to faster initiation of medical care and treatment. Important factor of the treatment is an interdisciplinary cooperation between specialist of dentistry and other doctors, especially a gastroenterologist and a surgeon.


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