Sağlıker sendromlu hastalarda işitme fonksiyonunun değerlendirilmesi

Bakır, Salih; Yıldız, İsmail; Sağlıker, Yahya
September 2009
Dicle Medical Journal / Dicle Tip Dergisi;2009, Vol. 36 Issue 3, p195
Academic Journal
Aim: The aim of this study was to evaluate th hearing functions of patients with Sagliker syndrome. Sagliker syndrome is a new disease entity that firstly has been described at year 2000. The frequency of this syndrome has been reported as approximately 0.5% of patient with chronic renal failure and mostly seen in poor and underdeveloped countries. The definite causes of this entity has not been not been clearly understood yet, however studies on risk factors that can lead to this syndrome are underway. Sagliker Syndrome seems to be related to chronic kidney disease and secondary hyperparathyroidism. Every kind of bone abnormalities including, skull deformities, short stature, maxillary and mandibulary changes, teeth abnormalities, soft and harmless tumoral tissues in the mouth and fingertip changes can develop. Psychological problems and depression may accompany these findings Materials and Methods: In present study, 12 patients with Sagliker Syndrome were retrospectively evaluated. Audiological tests were performed on these patients, including otoscopic examinations, Rinne and Weber tests, pure tone odiometry and timpanometry. Results: Five patients (41.7%) were found to have sensorineural type hearing loss. According to our results with a limited number of patients, hearing loss potential seems to be high with Sagliker Syndrome. Conclusion: Haemodialysis can be suggested as a risk factor on hearing loss of Sagliker syndrome, since all of our patients were on hemodialysis.


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