TITLE

Dyke Davidoff Masson Syndrome: A Case Report

AUTHOR(S)
Saini, H. Singh; Parakh, F. P.; Maheshwari, M.; Singh, G.; Karrer, V.; Aman, S.
PUB. DATE
October 2008
SOURCE
Neuroradiology Journal;Oct2008, Vol. 21 Issue 5, p678
SOURCE TYPE
Academic Journal
DOC. TYPE
Article
ABSTRACT
We describe a case of hemitrophy in a 12-year-old child presenting with seizures, hemiplegia and mental retardation. Hemiatrophy of one cerebral hemisphere is not frequently encountered in clinical practice. When this develops early in life (during the first two years), certain cranial changes like ipsilateral hypertrophy of the skull and sinuses occur. Asymmetry of cerebral hemispheric growth with atrophy on one side, ipsilateral osseous hypertrophy and hyper-pneumatization of sinuses with contralateral paresis are features of Dyke Davidoff Masson Syndrome (DDMS). Probably vascular occlusion was most important cause of hemiatrophy in our case.
ACCESSION #
37835967

 

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