Restricción del crecimiento intrauterino asociado a síndrome de Russell-Silver. A propósito de un caso

Limón, María Cristina Rangel; Domínguez, Luis Paulino Islas
October 2007
Revista Medica del Hospital General de Mexico;oct-dec2007, Vol. 70 Issue 4, p180
Academic Journal
The Russell-Silver syndrome has specific characteristics like restriction of intrauterine growth, typical fascies and corporal asymmetry, is a very rare genetic disease, is a pattern of malformations whose most characteristic features are intrauterine and postnatal growth retardation, a characteristic facial appearance and limb asymmetry. We notify a newborn, male of 39.5 weeks of gestation, who had physical characteristics compatible with Russell-Silver syndrome, weight of 1250 g, height 39 cm, cephalic perimeter 30 cm with restriction of the intrauterine growth. Father with this syndrome.


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