Polyarticular juvenile idiopathic arthritis associated with Fahr's syndrome

Dundar, U.; Solak, O.; Yigit, I.; Kavuncu, V.
July 2007
Journal of Pediatric Neurosciences;Jul-Dec2007, Vol. 2 Issue 2, p85
Academic Journal
Bilateral symmetric calcification involving striatum pallidum with or without deposits in the dentate nucleus, thalamus and white matter is commonly referred to as Fahr's syndrome. Symptoms of the disorder may include deterioration of motor function, spasticity, spastic paralysis, dysarthria, dementia, seizures, headache and athetosis. The clinical and imaging abnormalities are restricted to the central nervous system (CNS). We report an unusual association of Fahr's syndrome with polyarticular juvenile idiopathic arthritis in a girl.


Related Articles

  • Relationship between lesion location and the outcome of pallidotomy for Parkinson's disease. Yokochi, Fusako; Okiyama, Ryoichi; Taniguchi, Makoto; Takahashi, Hiroshi; Hasegawa, Naomi; Hamada, Ikuma // Journal of Neurology;Sep2001 Supplement 3, Vol. 248, p32 

    The relationships between lesion location and clinical outcome following posteroventral pallidotomy for Parkinson's disease were studied. Forty-four patients were operated forty-six times and studied with neurological and psychological examinations before and after pallidotomy. Lesion location...

  • Novel mutation of SLC20A2 in an Italian patient presenting with migraine. Rubino, Elisa; Giorgio, Elisa; Gallone, Salvatore; Pinessi, Lorenzo; Orsi, Laura; Gentile, Salvatore; Duca, Sergio; Brusco, Alfredo // Journal of Neurology;Oct2014, Vol. 261 Issue 10, p2019 

    The article presents a case study of a 48-year-old Italian woman with idiopathic basal ganglia calcifications associated with a novel mutation in the SLC20A2 gene and presented with episodic migraine. The recurrent attacks were characterized by pulsating pain of moderate intensity in...

  • Movement Disorders.  // Current Medical Literature: Neurology;2010, Vol. 26 Issue 2, p56 

    The article discusses clinical reviews on movement disorders. The article "The Role of DAT-SPECT in Movement Disorders" provides a review of the value of single-photon emission computed tomography to Parkinson's disease. It is believed that the information found in "Interruption of Deep Brain...

  • Neuronal discharge patterns in the Globus Pallidus pars interna in a patient with Parkinson's disease and hemiballismus secondary to subthalamotomy. Cerquetti, Daniel; Obeso, José; Merello, Marcelo // Experimental Brain Research;Sep2011, Vol. 213 Issue 4, p447 

    Alterations in the basal ganglia-thalamocortical 'motor' circuit activity, have been proposed to explain many features associated with hypokinetic and hyperkinetic movement disorders. We describe the firing pattern of the globus pallidus pars interna in a Parkinson disease's patient who...

  • Management of postoperative respiratory failure in a patient with acute diaphragmatic status dystonicus. Schumacher, J.; Wille, C.; Vesper, J. // BJA: The British Journal of Anaesthesia;Feb2012, Vol. 108 Issue 2, p329 

    No abstract available.

  • Pallidal Stimulation in Primary Dystonia Patients. Piboolnurak, Panida // Neurology Alert;Sep2008, Vol. 27 Issue 1, p2 

    ALTHOUGH DEEP BRAIN STIMULATION OF THE INTERNAL globus pallidus (GPi-DBS) is an effective treatment for patients with primary dystonia, there is no well defined outcome predictor of this treatment. To determine the predictors of the response to GPi-DBS, Isaias and colleagues retrospectively...

  • Pallidal deep brain stimulation relieves camptocormia in primary dystonia. Hagenacker, Tim; Gerwig, Marcus; Gasser, Thomas; Miller, Dorothea; Kastrup, Oliver; Jokisch, Daniel; Sure, Ulrich; Frings, Markus // Journal of Neurology;Jul2013, Vol. 260 Issue 7, p1833 

    Camptocormia, characterised by a forward flexion of the thoracolumbar spine may occur in various movement disorders, mainly in Parkinson's disease or in primary dystonia. In severe cases, patients with camptocormia are unable to walk. While treatment options are limited, deep brain stimulation...

  • Synaptogenesis in the Fetal Corpus Striatum, Globus Pallidus, and Substantia Nigra: Correlations With Striosomes of Graybiel and Dyskinesias in Premature Infants. Sarnat, Harvey B.; Auer, Roland N.; Flores-Sarnat, Laura // Journal of Child Neurology;Jan2013, Vol. 28 Issue 1, p60 

    Synaptogenesis can be detected in tissue sections by immunoreactivity for synaptophysin, a synaptic vesicle glycoprotein that serves as a marker of synaptic maturation. Reactivity was prospectively studied postmortem in sections of the striatum, globus pallidus, and substantia nigra in 172...

  • Pallidothalamic-projecting neurons in Macaca fascicularis co-express GABAergic and glutamatergic markers as seen in control, MPTP-treated and dyskinetic monkeys. Conte-Perales, Lorena; Rico, Alberto; Barroso-Chinea, Pedro; Gómez-Bautista, Virginia; Roda, Elvira; Luquin, Natasha; Sierra, Salvador; Lanciego, José // Brain Structure & Function;Nov2011, Vol. 216 Issue 4, p371 

    GABAergic neurons within the internal division of the globus pallidus (GPi) are the main source of basal ganglia output reaching the thalamic ventral nuclei in monkeys. Following dopaminergic denervation, pallidothalamic-projecting neurons are known to be hyperactive, whereas a reduction in GPi...


Read the Article


Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics