TITLE

Respiratory involvement in inherited primary muscle conditions

AUTHOR(S)
Shahrizaila, N.; Kinnear, W. J. M.; Wills, A. J.
PUB. DATE
October 2006
SOURCE
Journal of Neurology, Neurosurgery & Psychiatry;Oct2006, Vol. 77 Issue 10, p1108
SOURCE TYPE
Academic Journal
DOC. TYPE
Article
ABSTRACT
Patients with inherited muscle disorders can develop respiratory muscle weakness leading to ventilatory failure. Predicting the extent of respiratory involvement in the different types of inherited muscle disorders is important, as it allows clinicians to impart prognostic information and offers an opportunity for early interventional management strategies. The approach to respiratory assessment in patients with muscle disorders, the current knowledge of respiratory impairment in different muscle disorders and advice on the management of respiratory complications are summarised.
ACCESSION #
22853864

 

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