A case of torsion of a mucinous cystadenoma in triple-X syndrome with pure gonadal dysgenesis

Jeong-Heon Lee; Kwan-Sik Kim; Yong-Gon Cho
June 2006
Archives of Gynecology & Obstetrics;Jun2006, Vol. 274 Issue 3, p174
Academic Journal
Triple-X female characterized by primary amenorrhea and pure gonadal dysgenesis is extremely rare. We present a patient of triple-X syndrome who has not had menarche or the development of the secondary sexual characteristics. She had a hypoplastic uterus and streaked gonads on both sides with a twisted mucinous cystadenoma in the right adnexa.


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