Aortic atresia with aortico-left ventricular tunnel mimicking severe aortic incompetence in utero

Siepe, Matthias; Dittrich, Sven; Beyersdorf, Friedhelm; Schlensak, Christian
May 2006
European Journal of Cardio-Thoracic Surgery;May2006, Vol. 29 Issue 5, p845
Academic Journal
Abstract: A fetus was diagnosed with regurgitation from the aorta into the left ventricle. A large aortico-left ventricular tunnel with aortic atresia was identified postnatally by echocardiography in a neonate suffering from severe heart failure. We successfully reconstructed the valve and closed the tunnel with a patch on his first day of life. At three-month follow-up, the baby is asymptomatic with mild aortic regurgitation. The combination of congenital aortico-left ventricular tunnel and aortic atresia can be misinterpreted in prenatal echocardiography as aortic regurgitation. This pathology may require urgent operative interventions.


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