Cystic fibrosis presenting as acute upper airway obstruction

Davies, J.; Chaudry, R.; LaRovere, J.; Hansell, D.; Dawson, M.; Abrahamson, E.
January 2006
Thorax;Jan2006, Vol. 61 Issue 1, p92
Academic Journal
journal article
The article presents case report of a 2 year girl suffering with respiratory infections. Medical screening revealed that the girl has extensive surgical emphysema over her chest and neck. The chest radiograph revealed a pneumomediastinum. While being prepared for emergency intubation the symptoms began to resolve, allowing her to be managed conservatively without ventilation or chest drains. Computerized tomography showed a moderate anterior pneumomediastinum without a pneumothorax in addition to some bronchial wall thickening but no bronchiectasis. She has been diagnosed with cystic fibrosis on the basis of sweat testing and genetic analysis.


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