Repair of persistent truncus arteriosus with interrupted aortic arch

Tlaskal, Tomas; Hucin, Bohumil; Kucera, Vladimir; Vojtovic, Pavel; Gebauer, Roman; Chaloupecky, Vaclav; Skovranek, Jan
November 2005
European Journal of Cardio-Thoracic Surgery;Nov2005, Vol. 28 Issue 5, p736
Academic Journal
Abstract:: Objective: The aim of our study was to analyse experience with repair of truncus arteriosus with interrupted aortic arch. Methods: Between 1993 and 2004, eight consecutive patients underwent repair of truncus arteriosus with interrupted aortic arch. The median age was 6.5 days (range 1–85 days) and median weight was 3.2kg (range 2.6–4.8 kg). Five patients had type A and 3 patients had type B aortic arch interruption. The repair was performed in deep hypothermia with circulatory arrest in 4 patients and isolated selective low-flow perfusion of the head and the heart in the last 4 patients. The repair consisted in aortic arch reconstruction by direct anastomosis between descending and ascending aorta, closure of ventricular septal defect and reconstruction of the right ventricular to pulmonary artery continuity using a valved conduit. Results: One (12.5%) patient died from sepsis and hepato-renal failure 18 days after surgery. Seven (87.5%) patients were followed up for 2.0–11.7 years (median 2.6 years). No patient died after the discharge from hospital. In 4 patients 1–3 reinterventions were required 0.6–10.0 years after repair. Reoperations were performed for conduit obstruction in 2 patients, aortic regurgitation in 2 patients, right pulmonary artery stenosis in 2 patients and airway obstruction in 1 patient. In 2 patients concommitant aortic valve and conduit replacement was required. Balloon angioplasty for aortic arch obstruction was necessary in 1 patient, and for bilateral pulmonary branch stenosis in 1 patient. Five (28.6%) surviving patients are in NYHA class I and 2 (71.4%) patients are in NYHA class II. Conclusions: Primary repair of persistent truncus arteriosus with interrupted aortic arch can be done with low mortality and good mid-term results. Aortic arch reconstruction in isolated low-flow perfusion of the head and the heart influences favourably the postoperative recovery. The main postoperative problems are associated with conduit obstruction and aortic insufficiency.


Related Articles

  • Persistent truncus arteriosus with absence of right pulmonary artery. Wong, M.N.L.; Kirk, R.; Quek, S.C. // Heart;May2003, Vol. 89 Issue 5, p549 

    Describes a case of persistent truncus arteriosus in a 19-year-old girl. Failure of the x-ray to demonstrate the right pulmonary artery; Use of magnetic resonance angiography to define the pulmonary artery; Presence of two large aortopulmonary collateral vessels arising from the mid thoracic aorta.

  • High-Takeoff Single Coronary Artery With Intramural Course in Truncus Arteriosus: Prospective Echocardiographic Identification. Thankavel, Poonam; Brown, Paul; Nugent, Alan // Pediatric Cardiology;Aug2013, Vol. 34 Issue 6, p1517 

    The article presents a case study of a four month old child suffering from truncus arteriosus. It states that Transthoracic echocardiographic evaluation was conducted which stated that a short main pulmonary segment is developing from the leftward side of the trunk. It further informs about the...

  • Hemitruncus Presenting in an Adult. Edasery, B.; Sharma, M.; Vaddigiri, V.; Santucci, Jr, T. // Angiology;Oct1996, Vol. 47 Issue 10, p1023 

    Hemitruncus is a rare congenital anomaly in which one pulmonary artery branch, usually the right, arises from the ascending aorta just above the aortic sinuses, whereas the main pulmonary artery and the other pulmonary branch arise in their normal position. The authors present a case in which...

  • Echocardiography of common arterial trunk. Nguyen, Thieu; John, J. Blaine; Nardell, Kathryn; Gonzalez, Javier H.; Timofeev, Stan; Marx, Gerald // Cardiology in the Young;Dec2012, Vol. 22 Issue 6, p655 

    The article focuses on several components of two-dimensional echocardiography in newborn infants believed to have truncus arteriosus. It cites various goals of echocardiogram in neonates such as identifying the extent of a defect, assessment of the function of atrioventricular valves and...

  • Persistent Truncus Arteiosus With Double Aortic Arch and Mitral Stenosis. Imai, Kenta; Tsukuda, Kazuya; Sakazaki, Hisanori; Fujiwara, Keiichi // Pediatric Cardiology;Dec2013, Vol. 34 Issue 8, p2024 

    This report describes a case involving the rare combination of persistent truncus arteriosus type A2, double aortic arch, and mitral stenosis. At the age of 26 days, the patient underwent division of the right-sided aortic arch with tracheal compression and bilateral pulmonary banding. Fontan...

  • Common arterial trunk repair: with conduit or without? Raisky, Olivier; Ali, Walid Ben; Bajolle, Fanny; Marini, Davide; Metton, Olivier; Bonnet, Damien; Sidi, Daniel; Vouhé, Pascal R. // European Journal of Cardio-Thoracic Surgery;Oct2009, Vol. 36 Issue 4, p675 

    Abstract: Objective: To compare the mid-term results of two techniques used for the reconstruction of the pulmonary outflow tract during common arterial trunk repair in infancy, with special attention paid to re-operation rate and pulmonary arterial growth. Methods: Between 2000 and 2006, 32...

  • Long-term results after correction of persistent truncus arteriosus in 83 patients. Tlaskal, Tomas; Chaloupecky, Vaclav; Hucin, Bohumil; Gebauer, Roman; Krupickova, Sylvia; Reich, Oleg; Skovranek, Jan; Tax, Petr // European Journal of Cardio-Thoracic Surgery;Jun2010, Vol. 37 Issue 6, p1278 

    Abstract: Objective: This study aims to analyse long-term results after correction of truncus arteriosus in all patients operated in one institution over 28 years. Methods: Between 1981 and 2009, 83 patients, median age 54 days, underwent repair of truncus arteriosus. Interrupted aortic arch was...

  • A Case of Aortopulmonary Window Simulating Common Arterial Trunk Presented at the Age of 13. Çetin, İbrahim İlker; Örün, Utku Arman; Varan, Birgül; Coşkun, Mehmet; Tokel, Kürşad // CardioVascular & Interventional Radiology;Jul/Aug2005, Vol. 28 Issue 4, p533 

    We have reported a patient with aortopulmonary window (APW) simulating truncus. In classically defined APW, aorta and main pulmonary artery separate again after a distance from the window and form the aortic arch and pulmonary arteries. However, in our case, there was no separation and they...

  • Outcomes in patients with interrupted aortic arch and associated anomalies: a 20-year experience Brown, John W.; Ruzmetov, Mark; Okada, Yuji; Vijay, Palaniswamy; Rodefeld, Mark D.; Turrentine, Mark W. // European Journal of Cardio-Thoracic Surgery;May2006, Vol. 29 Issue 5, p666 

    Abstract: Objective: The surgical results for the repair of interrupted aortic arch (IAA) have evolved in recent years. We report our results for staged repair of this complex congenital malformation. Methods: Sixty-five patients (mean age, 16.9±41.7 days) were diagnosed with IAA and referred...


Read the Article


Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics