Early Onset of Childhood Pulmonary Lymphangiomyomatosis

Nussbaum, Eliezer; Groncy, Paula; Finklestein, Jerry; Dickman, Paul; Harrell III, James H.
June 1988
Clinical Pediatrics;Jun1988, Vol. 27 Issue 6, p279
Academic Journal
The authors present the first case of lymphangiomyomatosis in a pediatric patient. Radiographic findings, biopsy, computerized tomography, and electron microscopy were useful in detailing the presentation of early onset of pulmonary lymphangiomyomatosis. The unusual presentation of this child includes a description of her disease prior to any pulmonary symptomatology and 4 years of follow-up.


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