TITLE

Heart Block in Marfan's Syndrome

AUTHOR(S)
Keidar, Shlomo; Grenadier, Ehud; Cohen, Leon; Palant, Avraham
PUB. DATE
June 1981
SOURCE
Angiology;Jun1981, Vol. 32 Issue 6, p398
SOURCE TYPE
Academic Journal
DOC. TYPE
Article
ABSTRACT
Marfan's syndrome is classified as a heritable disorder of connective tissue in which the supporting structure is involved in clinical and pathologic alterations. In its classic form the syndrome is associated with abnormalities of the eye, aorta, and the skeleton. Conduction disturbances and ventricular arrhythmias have rarely been described in this syndrome. In this brief case report a patient with symptomatic heart block, prolonged atrial-His interval and ventricular arrhythmia in whom a permanent ventricular pacemaker has been implanted, is described.
ACCESSION #
16392302

 

Related Articles

  • MARFAN SYNDROME: The Silent Killer. Williams, Cheryl // USA Today Magazine;Nov89, Vol. 118 Issue 2534, p64 

    Focuses on the nature of the hereditary disorder called Marfan syndrome. Characteristics of the condition; Organs of the body affected by the condition; History of the discovery of the disease; Manifestations and symptoms of Marfan syndrome; Suspected cause of the condition; Tests that can be...

  • Undiagnosed complete congenital heart block - Obstetric and Neonatal Resuscitation Dilemma. Mukherjee, S.; Ramanan, R. // Perinatology: Journal of Perinatal & Neonatal Care;Nov2008, Vol. 10 Issue 6, p197 

    Here we report a case of complete congenital heart block resulting in unnecessary obstetric intervention in a mother with previously undiagnosed connective tissue disease . He was managed with epicardial pacing at 3 weeks and endocardial pacing at 3 months of age.

  • Reduced Activity of Serum �-Glucuronidase in Marfan Syndrome. Nakashima, Yasuhide // Angiology;Aug1986, Vol. 37 Issue 8, p576 

    Reduced activity of serum �-glucuronidase (EC 3.2.1.31) was found in three patients with Marfan syndrome, two of whom were siblings. The serum �-glu-curonidase levels in the patients ranged from 294 to 439 �g (360.7� 73.2, mean�SD) of the released P-nitrophenol/100 ml of...

  • Don't Miss the Signs of Marfan Syndrome.  // Review of Optometry;7/15/2012, Vol. 149 Issue 7, p12 

    The article presents information on a survey conducted by the National Marfan Foundation (NMF) according to which optometrists must become increasingly familiar with the early signs and symptoms of Marfan syndrome. It has been warned that Marfan syndrome may lead to aortic tear or rupture if not...

  • MARFAN SYNDROME. Nayak, U. S. Krishna; S., Ravikala.; Sebastian, Joseph // Guident;2012, Vol. 5 Issue 2, p63 

    The article offers an orthodontic perspective on the Marfan syndrome. It describes the syndrome as a genetic disorder of the connective tissue and affects people who are unusually tall, with long limbs and long, thin fingers. It also provides information on its etiology, classification, signs...

  • Republished: Marfan syndrome, inherited aortopathies and exercise: What is the right answer? Cheng, Andrew; Owens, David // Postgraduate Medical Journal;Jan2016, Vol. 92 Issue 1083, p51 

    Exercise recommendations for those who have Marfan syndrome or other genetic predisposition for thoracic aortic disease remain controversial and at times ambiguous. There are no outcomes studies to help guide recommendations. In this review, we examine the guidelines regarding exercise and...

  • Cardiovascular care of patients with Marfan syndrome. Nicholson, Christopher // Nursing Standard;3/16/2005, Vol. 19 Issue 27, p38 

    Marfan syndrome is a genetic disorder with potentially fatal cardiovascular complications. These risks can be reduced by early diagnosis, appropriate review and timely intervention. Care of patients with Marfan syndrome should be multidisciplinary and multiprofessional. This article reviews the...

  • Marfan Syndrome. Lake, Deborah Mann // HealthLeader Online Magazine;6/30/2010, p1 

    The article discusses the Marfan syndrome, a disorder of the connective tissue caused by a defect in a gene that controls a connective tissue protein. Symptoms of the disease include arm span greater than the height, flexible joints throughout the body and certain facial expressions. It most...

  • Marfan's Syndrome.  // Journal of Pediatric Ophthalmology & Strabismus;Mar/Apr2006, Vol. 43 Issue 2, p128 

    Presents images depicting Marfan's syndrome, including right eye with ectopia lentis, left eye with ectopia lentis and long fingers with joint hypermobility.

Share

Read the Article

Courtesy of VIRGINIA BEACH PUBLIC LIBRARY AND SYSTEM

Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics