Sharp, William V.
March 1971
Angiology;Mar1971, Vol. 22 Issue 3, p141
Academic Journal
This report concerns the study of a family with a high incidence of von Hippel's disease and associated pheochromocytoma. Five of nine children from a mother afflicted with the von Hippel's disease have developed pheochromocytomas. Four of these children have manifested von Hippel's disease. The appearance of pheochromocytoma at a young age, increased incidence of multiple tumors, and the decreased incidence of malignancy are emphasized in familial pheochromocytomas. A brief review of the literature of this phenomenon is included. The purpose of this report, is to again emphasize the occurrence of a curable form of hypertension in familial groups when associated with neurocutaneous ectodermal abnormalities.


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