Papaioannou, A.C.; Matsaniotis, N.; Cantez, T.; Durst, M.D.
October 1970
Angiology;Oct1970, Vol. 21 Issue 9, p580
Academic Journal
Eleven patients with Marfan syndrome from ages of 1 day to 21 years were studied. In one patient the development of cardiovascular complications is described from birth. In all cases the clinical and angiocardiographic findings were correlated. Auscultation appears to be the most useful clinical tool to suspect underlying cardiovascular lesions at a very early stage; angiocardiography is the only reliable laboratory method to confirm them. Specifically, the presence of a short systolic murmur over the apex with middle or late systolic accentuation, or a loud pulmonic closure are helpful auscultatory findings in this syndrome indicating the probable involvement of the mitral valve or of the media of the great vessels.


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