TITLE

THE SPECTRUM OF ARTERIOGRAPHIC FINDINGS IN OSLER--WEBER--RENDU DISEASE

AUTHOR(S)
Lande, Adam; Bedford, Alfred; Schechter, Lawrence S.
PUB. DATE
April 1976
SOURCE
Angiology;Apr1976, Vol. 27 Issue 4, p223
SOURCE TYPE
Academic Journal
DOC. TYPE
Article
ABSTRACT
In Osier-Weber-Rendu syndrome, visceral organs are frequently involved in addition to cutaneous and mucous membranous lesions. Detailed arteriographic investigation of 5 patients with this abnormality disclosed characteristic angiodysplastic lesions involving the lungs, liver, spleen, pancreas, gastrointestinal tract and mesentery. Arterial and aortic aneurysms appear to he an integral part of this abnormality. Common to angiodysplastic lesions is a variable degree of arteriovenous shunting. The arteriographic characteristics and the hemodynamic significance of major visceral arteriovenous shunts in hereditary hemorrhagic telangiectasia are discussed.
ACCESSION #
16352824

 

Related Articles

  • Whole-body MR vascular screening detects unsuspected concomitant vascular disease in coronary heart disease patients. Ladd, Susanne C.; Debatin, Joerg F.; Stang, Andreas; Bromen, Katja; Moebus, Susanne; Nuefer, Michael; Gizewski, Elke; Wanke, Isabel; Doerfler, Arnd; Ladd, Mark E.; Benemann, Jens; Erbel, Raimund; Forsting, Michael; Schmermund, Axel; Jöckel, Karl-Heinz // European Radiology;Apr2007, Vol. 17 Issue 4, p1035 

    Coronary heart disease (CHD) patients often show atherosclerotic vascular disease in other vascular territories. We evaluated how often whole-body MR imaging detects concomitant arterial pathologies in CHD patients, and how often these pathologies were not known to the patients previously. Of...

  • Hereditary Hemorrhagic Telangiectasia: The Rendu-Weber-Osler Syndrome. Gorlin, Robert J.; Sedano, Heddie O. // Journal of Dermatologic Surgery & Oncology;Nov78, Vol. 4 Issue 11, p864 

    The article presents information on Rendu-Weber-Osler Syndrome. This syndrome is characterized by familial occurrence of numerous telangiectasia on the skin and mucous membranes and repeated episodes of hemorrhage. An affected individual often is pale because of frequent loss of blood and...

  • Transcatheter Embolization of Hepatic Arteriovenous Fistula in Osler-Weber-Rendu Disease -- A Case Report. Roman, Cecelia F.; Se Do Cha; Incarvito, John; Cope, Constantin; Maranhao, Vladir // Angiology;Jun1987, Vol. 38 Issue 6, p484 

    Hereditary hemorrhagic telangiectasia (Osier-Weber-Rendu disease) is associated with arteriovenous fistulas throughout the body that can cause hemodynamic abnormalities. Owing to their size and extent, surgical repair is often not feasible. A patient referred for presumed valvular heart disease...

  • LIVER FAILURE CAUSED BY HEPATIC ANGIODYSPLASIA IN HEREDITARY HEMORRHAGIC TELANGIECTASIA. Mukasa, Chizu; Nakamura, Kazuhiko; Chijiiwa, Yoshiharu; Sakai, Hironori; Nawata, Hajime // American Journal of Gastroenterology;Mar1998, Vol. 93 Issue 3, p471 

    Hereditary hemorrhagic telangiectasia is a systemic vascular disease with autosomal dominant inheritance that results in telangiectasia, arteriovenous malformations, and hemangiomas. The liver is one of the organs commonly affected in hereditary hemorrhagic telangiectasia, and hepatic lesions...

  • Congenital Vascular Abnormalities in Okihiro's Syndrome -- A Case Report. Rashad, Fouad; Keith, Michael W.; Shields, Robert; Barre, Peter S.; Sobel, Mark // Angiology;Aug1987, Vol. 38 Issue 8, p642 

    In this report, the authors describe the angiographic findings in the forearm and hand in Okihiro's syndrome. To the best of their knowledge, it has not been described before. Okihiro et al described hypoplasia of the thenar eminence in association with a congenital disorder of ocular motility...

  • Parkes Weber or Klippel-Trenaunay syndrome? Non-invasive diagnosis with MR projection angiography. Ziyeh, S.; Spreer, J.; Rössler, J.; Strecker, R.; Hochmuth, A.; Schumacher, M.; Klisch, J. // European Radiology;Nov2004, Vol. 14 Issue 11, p2025 

    Klippel-Trenaunay and Parkes Weber (Klippel-Trenaunay-Weber) syndromes consist of vascular malformations of the capillary, venous and lymphatic systems combined with soft tissue and bone hypertrophy of the affected extremity. Klippel-Trenaunay syndrome is a pure low-flow condition, while Parkes...

  • Cerebral capillary telangiectasias: a meta-analysis and review of the literature. Gross, Bradley; Puri, Ajit; Popp, A.; Du, Rose // Neurosurgical Review;Apr2013, Vol. 36 Issue 2, p187 

    As a result of their presumed benign natural history, cerebral capillary telangiectasias (CCTs) are infrequently addressed in the neurosurgical literature. We performed a comprehensive review of CCTs via the PubMed database to synthesize overall epidemiological, radiographic, natural history,...

  • MESENTERIC VASCULAR INSUFFICIENCY. Baum, Stanley // American Journal of Gastroenterology;Jun1966, Vol. 45 Issue 6, p481 

    Comments on the mesenteric vascular insufficiency. Recognition of the importance of vascular supply of organs and systems of the body; Importance aspects of mesenteric angiography; Correlation between physiologic and arteriographic criteria.

  • Angiography of Hepatic Vascular Malformations Associated with Hereditary Hemorrhagic Telangiectasia. Manabu Hashimoto; Etuko Tate; Toshiaki Nishii; Jiro Watarai; Takanobu Shioya; Robert I. White // CardioVascular & Interventional Radiology;Mar/Apr2003, Vol. 26 Issue 2, p177 

    Purpose: To describe the angiographic features of hepatic involvement in hereditary hemorrhagic telangiectasia (HHT), particularly the presence of portovenous shunts. Methods: We reviewed the angiographic findings of seven patients with HHT. The patients comprised three women and four men with a...

Share

Read the Article

Courtesy of VIRGINIA BEACH PUBLIC LIBRARY AND SYSTEM

Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics