Pure red cell aplasia and adult-onset Still’s disease

Jae-Wook Chung; Yu-Jin Suh; Hyun-Ju Song; Jeong-Hee Choi; Hae-Sim Park; Sung-Ran Cho; Chang-Hee Suh
August 2004
Clinical Rheumatology;Aug2004, Vol. 23 Issue 4, p368
Academic Journal
Pure red cell aplasia (PRCA) associated with adult-onset Still’s disease (AOSD) is very rare. In this report a 28-year-old woman was admitted with fever, skin rash, jaundice and anemia. She was diagnosed as having AOSD with PRCA by bone marrow examination. Treatment with high-dose prednisolone and intravenous immunoglobulin resulted in remission of the PRCA and a good response of the AOSD.


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