April 2004
Gut;Apr2004 Supplement 3, Vol. 53, pA90
Academic Journal
The article presents outcomes in patients with cystic fibrosis and variceal haemorrhage. Autopsy and imaging studies show that liver involvement is common in cystic fibrosis. Complications of liver disease, however, are reported in less than 5 percent and variceal haemorrhage is uncommon. The impact of variceal haemorrhage on prognosis in cystic fibrosis is unclear. Because of this uncertainty patients have been recommended for liver transplantation (if pulmonary function is preserved) or for heart/lung/liver transplantation in preference to heart/lung transplantation on the basis of a history of variceal haemorrhage.


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