Peribiliary cysts have at least two different pathogeneses

Nakanuma, Yasuni
April 2004
Journal of Gastroenterology;2004, Vol. 39 Issue 4, p407
Academic Journal
There are several kinds of grossly visible cysts within the liver. Some are neoplastic cysts such as hepatobiliary cystadenoma and cystadenocarcinoma; others include congenital or developmental origins. Currently, these cysts are easily detectable by advanced imaging modalities. Polycystic liver diseases with autosomal dominant polycystic kidney disease or alone and solitary simple liver cysts are well-known cystic diseases of the liver, and there have been many clinico-pathological and genetic studies on these diseases. Multiple hepatic peribiliary cysts are the latest discovery in this field and were originally found in advanced liver diseases and also portal hypertensive liver diseases.


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