Knight, R S G; Will, R G
March 2004
Journal of Neurology, Neurosurgery & Psychiatry;Mar2004 Supplement 1, Vol. 75, pi36
Academic Journal
Prion diseases or transmissible spongiform encephalopathies (table 1) are characterised by the deposition of PrPSc, an abnormal form of a normal cellular protein, PrPC. These diseases exist in sporadic (idiopathic), genetic, and acquired forms.


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