Hyperinsulinism and Beckwith-Wiedemann syndrome

Munns, C. F.J.; Batch, J. A.
January 2001
Archives of Disease in Childhood -- Fetal & Neonatal Edition;Jan2001, Vol. 84 Issue 1, p67
Academic Journal
Beckwith-Wiedemann syndrome (BWS) uncommon cause of neonatal hyperinsulinaemic hypoglycemia. To improve understanding of researchers hypoglycemia in BWS, a comparison of this condition with the more well defined causes of neonatal hyperinsulinism was carried out. The other causes of neonatal hyperinsulinism can be divided into persistent hyperinsulinaemic hypoglycemia of infancy hyperinsulinism hyperammonaemia syndrome and transient hyperinsulinaemic hypoglycemia. There are many similarities between the hyperinsulinaemic hypoglycemia of BWS and other forms of neonatal hyperinsulinism.


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