A Case of Auditory Neuropathy with Recovery of Normal Hearing

Ji Hun Eom; Hyun Jung Min; Seung Hwan Lee; Ho Ki Lee
December 2013
Korean Journal of Audiology;Dec2013, Vol. 17 Issue 3, p138
Academic Journal
Newborn hearing screening test is very important in the early diagnosis of childhood hearing loss because it affects language development. Auditory neuropathy is a spectrum disorder characterized by abnormal auditory brainstem response but preserved otoacoustic emission and cochlear microphonics. In general, auditory neuropathy patients have poor word discrimination and variable patterns of pure tone audiometry. We report on a patient with auditory neuropathy diagnosed at 16 months of age and started wearing hearing aids, but showed normal pure tone and speech audiometric findings 3 years later. Close follow-up for patients with auditory neuropathy is recommended.


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